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HMBS Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech
Rabbit Polyclonal Antibody
Merk: Proteintech 14797-1-AP-20UL
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Beschrijving
PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.Specificatie
| HMBS | |
| Polyclonal | |
| Unconjugated | |
| HMBS | |
| HMBS, hydroxymethylbilane synthase, PBG D, PBGD, Porphobilinogen deaminase, Pre uroporphyrinogen synthase, UPS | |
| Rabbit | |
| Antigen Affinity Chromatography | |
| RUO | |
| 15288, 25709, 3145 | |
| -20°C | |
| Liquid |
| Immunocytochemistry, Western Blot, Immunoprecipitation, Immunofluorescence | |
| 0.2 mg/mL | |
| PBS with 50% glycerol and 0.02% sodium azide; pH 7.3 | |
| P08397, P19356, P22907 | |
| Hmbs | |
| HMBS Fusion Protein Ag6509 | |
| 20 μL | |
| Primary | |
| Mouse, Rat, Human | |
| Antibody | |
| IgG |
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