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  6. HMBS Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech

HMBS Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech

Rabbit Polyclonal Antibody

145.00 - 410.00

Specificatie

Antigeen HMBS
Concentratie 0.2 mg/mL
Toepassingen Immunocytochemistry, Western Blot, Immunoprecipitation, Immunofluorescence
Classificatie Polyclonal
Conjugaat Unconjugated
Meer specificaties weergeven

Producten 2
Produktcode Merk Aantal Prijs Hoeveelheid en beschikbaarheid  
Produktcode Merk Aantal Prijs Hoeveelheid en beschikbaarheid  
16803624
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Proteintech
14797-1-AP-20UL 		20 μL
145.00
20µL
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16893614
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Proteintech
14797-1-AP-150UL 		150 μL
410.00
150µL
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Beschrijving

Beschrijving

PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.
Specificatie

Specificatie

HMBS
Immunocytochemistry, Western Blot, Immunoprecipitation, Immunofluorescence
Unconjugated
Rabbit
Mouse, Rat, Human
P08397, P19356, P22907
15288, 25709, 3145
HMBS Fusion Protein Ag6509
Primary
-20°C
HMBS
0.2 mg/mL
Polyclonal
Liquid
RUO
PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
HMBS, hydroxymethylbilane synthase, PBG D, PBGD, Porphobilinogen deaminase, Pre uroporphyrinogen synthase, UPS
Hmbs
IgG
Antigen Affinity Chromatography
Antibody
Video's
SDS
Documentatie

Documentatie

Product Certifications
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